4. Clinical case of biplastic correction of abnormal pulmonary vein drainage with sinus venosus defect in a dominant innominate vein in adolescence

Authors

  • K.N. Kuatbekov Surgery, Center for Modern Medicine «Mediterra» LLP «Institute of Surgery», Almaty, Kazakhstan, современной медицины «Mediterra» ТОО «Институт хирургии», г. Алма- ты, Казахстан
  • A.L. Egizekov Surgery, Center for Modern Medicine «Mediterra» LLP «Institute of Surgery», Almaty, Kazakhstan, современной медицины «Mediterra» ТОО «Институт хирургии», г. Алма- ты, Казахстан
  • A.V. Mishin Surgery, Center for Modern Medicine «Mediterra» LLP «Institute of Surgery», Almaty, Kazakhstan, современной медицины «Mediterra» ТОО «Институт хирургии», г. Алма- ты, Казахстан
  • N.B. Baizhigitov Surgery, Center for Modern Medicine «Mediterra» LLP «Institute of Surgery», Almaty, Kazakhstan, современной медицины «Mediterra» ТОО «Институт хирургии», г. Алма- ты, Казахстан
  • B.Y. Suieubekov Surgery, Center for Modern Medicine «Mediterra» LLP «Institute of Surgery», Almaty, Kazakhstan, современной медицины «Mediterra» ТОО «Институт хирургии», г. Алма- ты, Казахстан
  • A.M. Nurbekov Surgery, Center for Modern Medicine «Mediterra» LLP «Institute of Surgery», Almaty, Kazakhstan, современной медицины «Mediterra» ТОО «Институт хирургии», г. Алма- ты, Казахстан

Downloads

Abstract

Sinus venosus defectis an unusual type of interatrial communication and is almost always combined with partial abnormal pulmonary vein drainage (PAPVD) into the superior vena cava (SVC) or right atrium (RA). Different types of venous outflow through the vena cava occur: the presence of an additional left vena cava with different drainage loci to both right and left atriaor, as in our case, the dominant unpaired vein directly draining into the right atrium with outprior communication with the superior right vena cava. This paper describes a clinical case of radical correction of partial anomalous pulmonary vein drainage combined with sinus venosus atrial septal defect (ASD) in a 14-year-old child with dominant venous outflow from the upper half of the body via innominate vein, by combined biplasty from auto pericardial patches, showing adequate upper-venous outflow under cardiopulmonary bypass. It is necessary to provide clear information about congenital heart disease and optimal timing of its surgical correction to a wide audience, not only to the professional medical community, but importantly, to the entire population of the Republic. The provision of publicly available professional information should be highlighted on the official websites of clinics and all available media opportunities, where parents and patients could be fully acquainted with the specific soft entire treatment processing an accessible and convenient information platform.

Keywords

partial anomalous pulmonary vein drainage, sinus venosus defect, clinical case, congenital heart disease, heart surgery

References

  1. Gotsman MS, Astley R, Parsons CC. Partial anomalous pulmonary venous drainage in association with atrial septal defect. Br Heart J 1965;27:566_571
  2. Mc Cormack RJM, Marquis RM, Julian DC, Griffiths HWC. Partial anomalous pulmonary venous drainage and its surgical correction. Scott Med J1960;5:367_381
  3. Hsu HM, Chang YT, Su WJ, Chu JJ, Chang YS, Hwang MS. The morphogenesis and associated anomalous pulmonary venous drainage in sinus venosus defect. Pediatr Neonatol. 2020 Feb;61(1):92-99. doi:10.1016/j.pedneo.2019.06.013.epub2019Jul4.PMID:31362863
  4. Rees S, Tahir M, Ahmad SJ, Subkovas E. Rare case of right ventricular dilatation associated with anomalous pulmonary venous drainage, sinus venosus atrial septal defect and persistent left superior vena cava. BMJ Case Rep. 2021 Jan 11;14(1):e239687. doi:10.1136/bcr-2020-239687.PMID:33431524;PMCID:PMC7802694
  5. Brody H. Drainage of the pulmonary veins into the right side of the heart. ArchPathol1942;33:221_240
  6. Relan J, Gupta SK, Rajagopal R, Ramakrishnan S, Gulati GS, Kothari SS, Saxena A,Sharma S, Rajashekar P, Anderson RH. Clarifying the anatomy of the superior sinusvenosus defect. Heart.2022 May;108(9):689-694. doi:10.1136/heartjnl-2021-319334.Epub2021Aug20.PMID:34417206
  7. Saxena A, Relan J, Agarwa lR, Awasthy N, Azad S, Chakrabarty M, Dagar KS, Devagourou V, Dharan BS, Gupta SK, Iyer KS, Jayranganath M, Joshi R, Kannan B, Katewa A, Kohli V, Kothari SS, Krishnamoorthy KM, Kulkarni S, Kumar RM, Kumar RK, Maheshwari S,ManoharK, Marwah A, Mishra S, Mohanty SR, Murthy KS, Rao KN, Suresh PV, Radhakrishnan S,Rajashekar P, Ramakrishnan S, Rao N, Rao SG, Chinnaswamy Reddy HM, Sharma R, Shivaprakash K, Subramanyan R, Kumar RS, Talwar S,Tomar M, Verma S, Vijaykumar R. Indian guidelines for indications and timing of intervention for common congenital heart diseases: Revised and updated consensusstatement of the Working group on management of congenital heart diseases. Ann PediatrCardiol. 2019 Sep-Dec;12(3):254-286. doi:10.4103/apc.APC_32_19.PMID:31516283;PMCID:PMC6716301
  8. Ng LY, Nolke L, James A, Grant B, Franklin O, Redmond JM, McGuinness J, Walsh K, McMahon CJ. Multimodality imaging in delineation of complex sinus venosus defects and treatment outcomes over the last decade. Cardiol Young. 2022 Jul;32(7):1112-1120. doi:10.1017/S1047951121003851.Epub2021Sep15.PMID:34521491
  9. Tretter JT, Chikkabyrappa S, Spicer DE, Backer CL, Mosca RS, Anderson RH, Bhatla P. Understanding the spectrum of sinus venosus interatrial communications. Cardiol Young. 2017 Apr;27(3):418-426. doi:10.1017/S1047951116000664.Epub2016May10.PMID:27161562
  10. Chowdhury UK, Anderson RH, George N, Singh S, Sankhyan LK, Gayatri SB, Malik V, Gharde P, Sengupta S. A Review of the Surgical Management of Anomalous Connection of the Right Superior Caval Vein to the Morphologically Left Atrium and Biatrial Drainage of Right Superior Caval Vein. World J Pediatr Congenit Heart Surg. 2020 Jul;11(4):466-484. doi:10.1177/2150135120912677.PMID:32645787

Published

2022-10-10

Issue

No. 3 (2022)

Section

Статьи