5. Hypertrophic cardiomyopathy. Literature review

Authors

  • CARDIOMYOPATHY. HYPERTROPHIC Scientific Center for Surgery” JSC, Almaty, Kazakhstan, Сызганова», г. Алматы, Казахстан
  • CARDIOMYOPATHY. HYPERTROPHIC Scientific Center for Surgery” JSC, Almaty, Kazakhstan, Сызганова», г. Алматы, Казахстан
  • I.Y. Sagatov Scientific Center for Surgery” JSC, Almaty, Kazakhstan, Сызганова», г. Алматы, Казахстан
  • B.M. Momynov Scientific Center for Surgery” JSC, Almaty, Kazakhstan, Сызганова», г. Алматы, Казахстан

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Abstract

Hypertrophic cardiomyopathy is a common hereditary heart disease with a heterogeneous clinical picture and a natural history. Recent advances in diagnosis and treatment methods have played an important role in reducing the incidence of adverse clinical events; however, the complete elimination of sudden cardiac death is still an unattainable achievement. Despite the heterogeneous clinical profile and complex pathophysiology, effective treatment strategies are available, including implantable defibrillators to prevent sudden death, medical and surgical myectomy (or, alternatively, alcohol ablation of the septum) to alleviate outflow obstruction and symptoms of heart failure, as well as pharmacological strategies (and possibly radiofrequency ablation) to control atrial fibrillation and prevent embolic stroke. Now, after more than 50 years, hypertrophic cardiomyopathy has been transformed from a rare and largely untreatable disorder to a common genetic disease with management strategies that permit realistic aspirations for restored quality of life and advanced longevity. This article discusses some aspects of this condition: epidemiology, clinic, diagnosis and surgery technique.

Objective. Evaluate the effectiveness of surgical treatment of patients with hypertrophic cardiomyopathy.

Material and methods. This literature review was carried out in accordance with the PRISM statement. The databases searched in this review included Pubmed, Web of Science, Scopus, and Cochrane for systematic reviews.

Conclusion. The diagnosis of HCMP is based mainly on echocardiographic variables including the dynamic parameters of LV, LVOT the distribution of increased muscle thickness, the mechanism and severity of MR as well as the degree of diastolic dysfunction.

Keywords

HCMP, echocardiography, left ventricle

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Published

2022-03-02

Issue

No. 1 (2022)

Section

Статьи